Annotation Detail

Information
Associated Genes
MYH7
Associated Variants
MYH7 p.Arg719Trp (p.R719W) ( ENST00000355349.4, ENST00000713768.1, ENST00000713769.1 )
MYH7 p.Arg719Trp (p.R719W) ( ENST00000355349.4, ENST00000713768.1, ENST00000713769.1 )
Associated Disease
hypertrophic cardiomyopathy 1
Source Database
ClinVar
Description
NM_000257.4(MYH7):c.2155C>T (p.Arg719Trp) AND Hypertrophic cardiomyopathy 1
ClinVar Allele ID
29143
ClinVar RefSeq Alternation Syntax
NM_000257.4:c.2155C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-04-16
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000015160
ClinVar Disease
Hypertrophic cardiomyopathy 1
Observed Origin Sample
germline
Pubmed
9544842
Pubmed
8282798
Drugs