Annotation Detail

Information
Associated Genes
MYH7
Associated Variants
MYH7 p.Arg403Gln (p.R403Q) ( ENST00000355349.4, ENST00000713768.1, ENST00000713769.1 )
MYH7 p.Arg403Gln (p.R403Q) ( ENST00000355349.4, ENST00000713768.1, ENST00000713769.1 )
Associated Disease
hypertrophic cardiomyopathy 1
Source Database
ClinVar
Description
NM_000257.4(MYH7):c.1208G>A (p.Arg403Gln) AND Hypertrophic cardiomyopathy 1
ClinVar Allele ID
29126
ClinVar RefSeq Alternation Syntax
NM_000257.4:c.1208G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-08-01
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000015143
ClinVar Disease
Hypertrophic cardiomyopathy 1
Observed Origin Sample
germline
Pubmed
1975517
Pubmed
12601548
Pubmed
2249844
Pubmed
9541509
Pubmed
21239280
Pubmed
13732753
Pubmed
7994801
Pubmed
1634614
Pubmed
9140839
Drugs