Annotation Detail

Information
Associated Genes
SNCA
Associated Variants
SNCA p.Ala30Pro (p.A30P) ( ENST00000336904.7, ENST00000345009.8, ENST00000394986.5, ENST00000394989.6, ENST00000394991.8, ENST00000420646.6, ENST00000502987.5, ENST00000505199.5, ENST00000506244.5, ENST00000508895.5, ENST00000611107.1, ENST00000618500.4, ENST00000673718.1, ENST00000673902.1, ENST00000674129.1 )
SNCA p.Ala30Pro (p.A30P) ( ENST00000336904.7, ENST00000345009.8, ENST00000394986.5, ENST00000394989.6, ENST00000394991.8, ENST00000420646.6, ENST00000502987.5, ENST00000505199.5, ENST00000506244.5, ENST00000508895.5, ENST00000611107.1, ENST00000618500.4, ENST00000673718.1, ENST00000673902.1, ENST00000674129.1 )
Associated Disease
Autosomal dominant Parkinson disease 1
Source Database
ClinVar
Description
NM_000345.4(SNCA):c.88G>C (p.Ala30Pro) AND Autosomal dominant Parkinson disease 1
ClinVar Allele ID
29047
ClinVar RefSeq Alternation Syntax
NM_001375287.1:c.88G>C
ClinVar RefSeq Alternation Syntax
NR_164675.1:n.313G>C
ClinVar RefSeq Alternation Syntax
NM_001375288.1:c.88G>C
ClinVar RefSeq Alternation Syntax
NM_000345.4:c.88G>C
ClinVar RefSeq Alternation Syntax
NM_001146054.2:c.88G>C
ClinVar RefSeq Alternation Syntax
NM_007308.3:c.88G>C
ClinVar RefSeq Alternation Syntax
NR_164674.1:n.166G>C
ClinVar RefSeq Alternation Syntax
NM_001375285.1:c.88G>C
ClinVar RefSeq Alternation Syntax
NM_001146055.2:c.88G>C
ClinVar RefSeq Alternation Syntax
NM_001375286.1:c.88G>C
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2020-11-20
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000015045
ClinVar Disease
Autosomal dominant Parkinson disease 1
Observed Origin Sample
germline
Pubmed
24158909
Pubmed
20437567
Pubmed
24158904
Pubmed
9462735
Pubmed
11376188
Drugs