Annotation Detail

Information
Associated Genes
RET
Associated Variants
RET p.Arg114His (p.R114H) ( ENST00000340058.6, ENST00000355710.8, ENST00000615310.5, ENST00000638465.2, ENST00000640619.2, ENST00000683278.2, ENST00000684216.2, ENST00000713926.1 )
RET p.Arg114His (p.R114H) ( ENST00000340058.6, ENST00000355710.8, ENST00000615310.5, ENST00000638465.2, ENST00000640619.2, ENST00000683278.2, ENST00000684216.2, ENST00000713926.1 )
Associated Disease
Congenital central hypoventilation
Source Database
ClinVar
Description
NM_020975.6(RET):c.341G>A (p.Arg114His) AND Congenital central hypoventilation
ClinVar Allele ID
28986
ClinVar RefSeq Alternation Syntax
NM_001406771.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_000323.2:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406763.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406769.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406773.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406744.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406781.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406787.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406779.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_020975.6:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406780.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406785.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406760.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_020629.2:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406765.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406759.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406772.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_020630.7:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406743.1:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_001406782.1:c.341G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2002-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014974
ClinVar Disease
Congenital central hypoventilation
Observed Origin Sample
germline
Pubmed
12086152
Drugs