Annotation Detail

Information
Associated Genes
PTH1R
Associated Variants
PTH1R p.Ile458Arg (p.I458R) ( ENST00000313049.9, ENST00000418619.5, ENST00000430002.6, ENST00000449590.6 )
PTH1R p.Ile458Arg (p.I458R) ( ENST00000313049.9, ENST00000418619.5, ENST00000430002.6, ENST00000449590.6 )
Associated Disease
Metaphyseal chondrodysplasia, Jansen type
Source Database
ClinVar
Description
NM_000316.3(PTH1R):c.1373T>G (p.Ile458Arg) AND Metaphyseal chondrodysplasia, Jansen type
ClinVar Allele ID
28786
ClinVar RefSeq Alternation Syntax
NM_000316.3:c.1373T>G
ClinVar RefSeq Alternation Syntax
NM_001184744.1:c.1373T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1996-09-05
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014754
ClinVar Disease
Metaphyseal chondrodysplasia, Jansen type
Observed Origin Sample
germline
Pubmed
8703170
Drugs