Annotation Detail

Information
Associated Genes
PTH1R
Associated Variants
PTH1R p.Thr410Pro (p.T410P) ( ENST00000313049.9, ENST00000418619.5, ENST00000430002.6, ENST00000449590.6 )
PTH1R p.Thr410Pro (p.T410P) ( ENST00000313049.9, ENST00000418619.5, ENST00000430002.6, ENST00000449590.6 )
Associated Disease
Metaphyseal chondrodysplasia, Jansen type
Source Database
ClinVar
Description
NM_000316.3(PTH1R):c.1228A>C (p.Thr410Pro) AND Metaphyseal chondrodysplasia, Jansen type
ClinVar Allele ID
28782
ClinVar RefSeq Alternation Syntax
NM_000316.3:c.1228A>C
ClinVar RefSeq Alternation Syntax
NM_001184744.1:c.1228A>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1999-09-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014750
ClinVar Disease
Metaphyseal chondrodysplasia, Jansen type
Observed Origin Sample
germline
Pubmed
10487664
Drugs