Annotation Detail

Information
Associated Genes
PPARA
Associated Variants
PPARA p.Leu162Val (p.L162V) ( ENST00000402126.2, ENST00000407236.6 )
PPARA p.Leu162Val (p.L162V) ( ENST00000402126.2, ENST00000407236.6 )
Associated Disease
Hyperapobetalipoproteinemia, susceptibility to
Source Database
ClinVar
Description
NM_005036.6(PPARA):c.484C>G (p.Leu162Val) AND Hyperapobetalipoproteinemia, susceptibility to
ClinVar Allele ID
28740
ClinVar RefSeq Alternation Syntax
NM_001393944.1:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001393945.1:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001001928.4:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_005036.6:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001393941.1:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001362872.2:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001362873.3:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001393946.1:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001393947.1:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001001929.3:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001393943.1:c.484C>G
ClinVar RefSeq Alternation Syntax
NM_001393942.1:c.484C>G
Clinical Significance Description
Benign
Clinical Significance Last Update
2004-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014700
ClinVar Disease
Hyperapobetalipoproteinemia, susceptibility to
Observed Origin Sample
germline
Pubmed
15309680
Pubmed
12006394
Pubmed
10828087
Drugs