Annotation Detail

Information
Associated Genes
ABCB4
Associated Variants
ABCB4 p.Thr175Ala (p.T175A) ( ENST00000265723.8, ENST00000359206.8, ENST00000453593.5, ENST00000649586.2 )
ABCB4 p.Thr175Ala (p.T175A) ( ENST00000265723.8, ENST00000359206.8, ENST00000453593.5, ENST00000649586.2 )
Associated Disease
Low phospholipid associated cholelithiasis
Source Database
ClinVar
Description
NM_000443.4(ABCB4):c.523A>G (p.Thr175Ala) AND Low phospholipid associated cholelithiasis
ClinVar Allele ID
28730
ClinVar RefSeq Alternation Syntax
NM_018849.3:c.523A>G
ClinVar RefSeq Alternation Syntax
NM_000443.4:c.523A>G
ClinVar RefSeq Alternation Syntax
NM_018850.3:c.523A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2001-05-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014690
ClinVar Disease
Low phospholipid associated cholelithiasis
Observed Origin Sample
germline
Pubmed
11313316
Drugs