Annotation Detail

Information
Associated Genes
ABCB4
Associated Variants
ABCB4 p.Ala546Asp (p.A546D) ( ENST00000265723.8, ENST00000359206.8, ENST00000453593.5, ENST00000649586.2 )
ABCB4 p.Ala546Asp (p.A546D) ( ENST00000265723.8, ENST00000359206.8, ENST00000453593.5, ENST00000649586.2 )
Associated Disease
Cholestasis, intrahepatic, of pregnancy, 3
Source Database
ClinVar
Description
NM_000443.4(ABCB4):c.1637C>A (p.Ala546Asp) AND Cholestasis, intrahepatic, of pregnancy, 3
ClinVar Allele ID
28728
ClinVar RefSeq Alternation Syntax
NM_018850.3:c.1637C>A
ClinVar RefSeq Alternation Syntax
NM_000443.4:c.1637C>A
ClinVar RefSeq Alternation Syntax
NM_018849.3:c.1637C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2000-05-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014687
ClinVar Disease
Cholestasis, intrahepatic, of pregnancy, 3
Observed Origin Sample
germline
Pubmed
10767346
Drugs