Annotation Detail

Information
Associated Genes
PDGFRA
Associated Variants
PDGFRA p.Thr674Ile (p.T674I), ENSG00000282278 p.Thr434Ile (p.T434I) ( ENST00000257290.10 )
PDGFRA p.Thr674Ile (p.T674I), ENSG00000282278 p.Thr434Ile (p.T434I) ( ENST00000257290.10 )
Associated Disease
Hypereosinophilic syndrome, idiopathic, resistant to imatinib
Source Database
ClinVar
Description
NM_006206.6(PDGFRA):c.2021C>T (p.Thr674Ile) AND Hypereosinophilic syndrome, idiopathic, resistant to imatinib
ClinVar Allele ID
28589
ClinVar RefSeq Alternation Syntax
NM_006206.6:c.2021C>T
ClinVar RefSeq Alternation Syntax
NM_001347827.2:c.2021C>T
ClinVar RefSeq Alternation Syntax
NM_001347830.2:c.2060C>T
ClinVar RefSeq Alternation Syntax
NM_001347829.2:c.2021C>T
ClinVar RefSeq Alternation Syntax
NM_001347828.2:c.2096C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2003-03-27
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014509
ClinVar Disease
Hypereosinophilic syndrome, idiopathic, resistant to imatinib
Observed Origin Sample
germline
Pubmed
12660384
Drugs