Annotation Detail

Information
Associated Genes
KCNE1
Associated Variants
KCNE1 p.Asp85Asn (p.D85N) ( ENST00000416357.6, ENST00000399284.1, ENST00000399286.3, ENST00000337385.7, ENST00000399289.7, ENST00000432085.5, ENST00000611936.1, ENST00000621601.4 )
KCNE1 p.Asp85Asn (p.D85N) ( ENST00000337385.7, ENST00000399284.1, ENST00000399286.3, ENST00000399289.7, ENST00000416357.6, ENST00000432085.5, ENST00000611936.1, ENST00000621601.4 )
Associated Disease
Long QT syndrome 5, acquired, susceptibility to
Source Database
ClinVar
Description
NM_000219.6(KCNE1):c.253G>A (p.Asp85Asn) AND Long QT syndrome 5, acquired, susceptibility to
ClinVar Allele ID
28518
ClinVar RefSeq Alternation Syntax
NM_001127670.4:c.253G>A
ClinVar RefSeq Alternation Syntax
NM_001270404.3:c.253G>A
ClinVar RefSeq Alternation Syntax
NM_001270402.3:c.253G>A
ClinVar RefSeq Alternation Syntax
NM_000219.6:c.253G>A
ClinVar RefSeq Alternation Syntax
NM_001270405.3:c.253G>A
ClinVar RefSeq Alternation Syntax
NM_001270403.2:c.253G>A
ClinVar RefSeq Alternation Syntax
NM_001127668.4:c.253G>A
ClinVar RefSeq Alternation Syntax
NM_001127669.4:c.253G>A
Clinical Significance Description
risk factor
Clinical Significance Last Update
2006-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014422
ClinVar Disease
Long QT syndrome 5, acquired, susceptibility to
Observed Origin Sample
germline
Pubmed
14760488
Pubmed
16823764
Pubmed
8899564
Pubmed
15051636
Drugs