Annotation Detail

Information
Associated Genes
TTR
Associated Variants
TTR p.Val91Ala (p.V91A) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
TTR p.Val91Ala (p.V91A) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
Associated Disease
Familial amyloid neuropathy
Source Database
ClinVar
Description
NM_000371.4(TTR):c.272T>C (p.Val91Ala) AND Familial amyloid neuropathy
ClinVar Allele ID
28484
ClinVar RefSeq Alternation Syntax
NM_000371.4:c.272T>C
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2022-11-28
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014387
ClinVar Disease
Familial amyloid neuropathy
Observed Origin Sample
germline
Pubmed
9017946
Pubmed
8257997
Drugs