Annotation Detail

Information
Associated Genes
TTR
Associated Variants
TTR p.Leu75Pro (p.L75P) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
TTR p.Leu75Pro (p.L75P) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
Associated Disease
Familial amyloid neuropathy
Source Database
ClinVar
Description
NM_000371.4(TTR):c.224T>C (p.Leu75Pro) AND Familial amyloid neuropathy
ClinVar Allele ID
28477
ClinVar RefSeq Alternation Syntax
NM_000371.4:c.224T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1997-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014380
ClinVar Disease
Familial amyloid neuropathy
Observed Origin Sample
germline
Pubmed
8218290
Pubmed
14404854
Pubmed
7910950
Pubmed
4952599
Pubmed
8990019
Pubmed
7018469
Drugs