Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Glu219Lys (p.E219K) ( ENST00000430350.2, ENST00000457586.2, ENST00000424424.2, ENST00000379440.9 )
PRNP p.Glu219Lys (p.E219K) ( ENST00000424424.2, ENST00000379440.9, ENST00000457586.2, ENST00000430350.2 )
Associated Disease
Protection against Creutzfeldt-Jakob disease
Source Database
ClinVar
Description
NM_000311.5(PRNP):c.655G>A (p.Glu219Lys) AND Protection against Creutzfeldt-Jakob disease
ClinVar Allele ID
28448
ClinVar RefSeq Alternation Syntax
NM_001080122.3:c.655G>A
ClinVar RefSeq Alternation Syntax
NM_001080121.3:c.655G>A
ClinVar RefSeq Alternation Syntax
NM_183079.4:c.655G>A
ClinVar RefSeq Alternation Syntax
NM_001080123.3:c.655G>A
ClinVar RefSeq Alternation Syntax
NM_000311.5:c.655G>A
ClinVar RefSeq Alternation Syntax
NM_001271561.3:c.*344G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2012-02-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014350
ClinVar Disease
Protection against Creutzfeldt-Jakob disease
Observed Origin Sample
germline
Pubmed
22108575
Pubmed
20697057
Pubmed
12815603
Pubmed
16217673
Pubmed
9482303
Pubmed
15557533
Drugs