Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Thr183Ala (p.T183A) ( ENST00000379440.9, ENST00000424424.2, ENST00000430350.2, ENST00000457586.2 )
PRNP p.Thr183Ala (p.T183A) ( ENST00000379440.9, ENST00000424424.2, ENST00000430350.2, ENST00000457586.2 )
Associated Disease
Spongiform encephalopathy with neuropsychiatric features
Source Database
ClinVar
Description
NM_000311.5(PRNP):c.547A>G (p.Thr183Ala) AND Spongiform encephalopathy with neuropsychiatric features
ClinVar Allele ID
28446
ClinVar RefSeq Alternation Syntax
NM_001080122.3:c.547A>G
ClinVar RefSeq Alternation Syntax
NM_001271561.3:c.*236A>G
ClinVar RefSeq Alternation Syntax
NM_183079.4:c.547A>G
ClinVar RefSeq Alternation Syntax
NM_000311.5:c.547A>G
ClinVar RefSeq Alternation Syntax
NM_001080123.3:c.547A>G
ClinVar RefSeq Alternation Syntax
NM_001080121.3:c.547A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1997-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014347
ClinVar Disease
Spongiform encephalopathy with neuropsychiatric features
Observed Origin Sample
germline
Pubmed
9266722
Drugs