Annotation Detail

Information
Associated Genes
PTPN11
Associated Variants
PTPN11 p.Glu76Val (p.E76V) ( ENST00000351677.7, ENST00000392597.5, ENST00000635625.1, ENST00000639857.2, ENST00000687906.1, ENST00000688597.1, ENST00000690210.1 )
PTPN11 p.Glu76Val (p.E76V) ( ENST00000351677.7, ENST00000392597.5, ENST00000635625.1, ENST00000639857.2, ENST00000687906.1, ENST00000688597.1, ENST00000690210.1 )
Associated Disease
juvenile myelomonocytic leukemia
Source Database
ClinVar
Description
NM_002834.5(PTPN11):c.227A>T (p.Glu76Val) AND Juvenile myelomonocytic leukemia
ClinVar Allele ID
28376
ClinVar RefSeq Alternation Syntax
NM_001330437.2:c.227A>T
ClinVar RefSeq Alternation Syntax
NM_002834.5:c.227A>T
ClinVar RefSeq Alternation Syntax
NM_001374625.1:c.224A>T
ClinVar RefSeq Alternation Syntax
NM_080601.3:c.227A>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2003-06-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014265
ClinVar Disease
Juvenile myelomonocytic leukemia
Observed Origin Sample
somatic
Pubmed
12717436
Drugs