Annotation Detail

Information
Associated Genes
KRAS
Associated Variants
KRAS p.Lys5Glu (p.K5E) ( ENST00000685328.1, ENST00000256078.10, ENST00000688940.1, ENST00000557334.6, ENST00000556131.2, ENST00000692768.1, ENST00000693229.1, ENST00000311936.8, ENST00000686969.1 )
KRAS p.Lys5Glu (p.K5E) ( ENST00000256078.10, ENST00000311936.8, ENST00000556131.2, ENST00000557334.6, ENST00000685328.1, ENST00000686969.1, ENST00000688940.1, ENST00000692768.1, ENST00000693229.1 )
Associated Disease
Noonan syndrome 3
Source Database
ClinVar
Description
NM_004985.5(KRAS):c.13A>G (p.Lys5Glu) AND Noonan syndrome 3
ClinVar Allele ID
27635
ClinVar RefSeq Alternation Syntax
NM_033360.4:c.13A>G
ClinVar RefSeq Alternation Syntax
NM_001369787.1:c.13A>G
ClinVar RefSeq Alternation Syntax
NM_004985.5:c.13A>G
ClinVar RefSeq Alternation Syntax
NM_001369786.1:c.13A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2020-06-11
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000013427
ClinVar Disease
Noonan syndrome 3
Observed Origin Sample
germline
Pubmed
18386799
Pubmed
22211815
Pubmed
17468812
Drugs