Annotation Detail

Information
Associated Genes
TNNI3
Associated Variants
TNNI3 p.Gly203Ser (p.G203S) ( ENST00000344887.10, ENST00000588882.1, ENST00000665070.1, ENST00000714236.1, ENST00000714237.1, ENST00000714238.1, ENST00000714240.1 )
TNNI3 p.Gly203Ser (p.G203S) ( ENST00000344887.10, ENST00000588882.1, ENST00000665070.1, ENST00000714236.1, ENST00000714237.1, ENST00000714238.1, ENST00000714240.1 )
Associated Disease
hypertrophic cardiomyopathy 7
Source Database
ClinVar
Description
NM_000363.5(TNNI3):c.607G>A (p.Gly203Ser) AND Hypertrophic cardiomyopathy 7
ClinVar Allele ID
27471
ClinVar RefSeq Alternation Syntax
NM_000363.5:c.607G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1997-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000013245
ClinVar Disease
Hypertrophic cardiomyopathy 7
Observed Origin Sample
germline
Pubmed
9241277
Drugs