Annotation Detail

Information
Associated Genes
TNNI3
Associated Variants
TNNI3 p.Ala2Val (p.A2V) ( ENST00000344887.10, ENST00000665070.1, ENST00000714236.1, ENST00000714237.1, ENST00000714238.1 )
TNNI3 p.Ala2Val (p.A2V) ( ENST00000344887.10, ENST00000665070.1, ENST00000714236.1, ENST00000714237.1, ENST00000714238.1 )
Associated Disease
dilated cardiomyopathy 2A
Source Database
ClinVar
Description
NM_000363.5(TNNI3):c.5C>T (p.Ala2Val) AND Dilated cardiomyopathy 2A
ClinVar Allele ID
52567
ClinVar RefSeq Alternation Syntax
NM_000363.5:c.5C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2009-08-14
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000013240
ClinVar Disease
Dilated cardiomyopathy 2A
Observed Origin Sample
germline
Pubmed
15070570
Pubmed
19590045
Drugs