Annotation Detail

Information
Associated Genes
TNFRSF1A
Associated Variants
TNFRSF1A p.Cys99Ser (p.C99S) ( ENST00000162749.7, ENST00000440083.7, ENST00000540022.5 )
TNFRSF1A p.Cys99Ser (p.C99S) ( ENST00000162749.7, ENST00000440083.7, ENST00000540022.5 )
Associated Disease
TNF receptor-associated periodic fever syndrome (TRAPS)
Source Database
ClinVar
Description
NM_001065.4(TNFRSF1A):c.295T>A (p.Cys99Ser) AND TNF receptor-associated periodic fever syndrome (TRAPS)
ClinVar Allele ID
27384
ClinVar RefSeq Alternation Syntax
NM_001065.4:c.295T>A
ClinVar RefSeq Alternation Syntax
NM_001346092.2:c.-283T>A
ClinVar RefSeq Alternation Syntax
NM_001346091.2:c.-30T>A
ClinVar RefSeq Alternation Syntax
NR_144351.2:n.557T>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2003-09-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000013138
ClinVar Disease
TNF receptor-associated periodic fever syndrome (TRAPS)
Observed Origin Sample
germline
Observed Origin Sample
not provided
Pubmed
13130484
Drugs