Annotation Detail

Information
Associated Genes
TNFRSF1A
Associated Variants
TNFRSF1A p.Cys62Gly (p.C62G) ( ENST00000540022.5, ENST00000162749.7, ENST00000440083.7 )
TNFRSF1A p.Cys62Gly (p.C62G) ( ENST00000162749.7, ENST00000440083.7, ENST00000540022.5 )
Associated Disease
TNF receptor-associated periodic fever syndrome (TRAPS)
Source Database
ClinVar
Description
NM_001065.4(TNFRSF1A):c.184T>G (p.Cys62Gly) AND TNF receptor-associated periodic fever syndrome (TRAPS)
ClinVar Allele ID
27382
ClinVar RefSeq Alternation Syntax
NM_001346091.2:c.-131-235T>G
ClinVar RefSeq Alternation Syntax
NM_001065.4:c.184T>G
ClinVar RefSeq Alternation Syntax
NR_144351.2:n.446T>G
ClinVar RefSeq Alternation Syntax
NM_001346092.2:c.-394T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2001-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000013136
ClinVar Disease
TNF receptor-associated periodic fever syndrome (TRAPS)
Observed Origin Sample
germline
Observed Origin Sample
not provided
Pubmed
11443543
Drugs