Annotation Detail

Information
Associated Genes
TNFRSF1A
Associated Variants
TNFRSF1A p.Cys59Ser (p.C59S) ( ENST00000540022.5, ENST00000162749.7, ENST00000440083.7 )
TNFRSF1A p.Cys59Ser (p.C59S) ( ENST00000162749.7, ENST00000440083.7, ENST00000540022.5 )
Associated Disease
TNF receptor-associated periodic fever syndrome (TRAPS)
Source Database
ClinVar
Description
NM_001065.4(TNFRSF1A):c.176G>C (p.Cys59Ser) AND TNF receptor-associated periodic fever syndrome (TRAPS)
ClinVar Allele ID
27381
ClinVar RefSeq Alternation Syntax
NR_144351.2:n.438G>C
ClinVar RefSeq Alternation Syntax
NM_001065.4:c.176G>C
ClinVar RefSeq Alternation Syntax
NM_001346092.2:c.-402G>C
ClinVar RefSeq Alternation Syntax
NM_001346091.2:c.-131-243G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2020-09-09
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000013135
ClinVar Disease
TNF receptor-associated periodic fever syndrome (TRAPS)
Observed Origin Sample
germline
Observed Origin Sample
not provided
Pubmed
10902757
Pubmed
11443543
Drugs