Annotation Detail

Information
Associated Genes
IDUA
Associated Variants
IDUA p.Pro533Arg (p.P533R) ( ENST00000247933.9, ENST00000514224.2 )
IDUA p.Pro533Arg (p.P533R) ( ENST00000247933.9, ENST00000514224.2 )
Associated Disease
Hurler syndrome
Source Database
ClinVar
Description
NM_000203.5(IDUA):c.1598C>G (p.Pro533Arg) AND Hurler syndrome
ClinVar Allele ID
26949
ClinVar RefSeq Alternation Syntax
NM_000203.5:c.1598C>G
ClinVar RefSeq Alternation Syntax
NR_110313.1:n.1686C>G
ClinVar RefSeq Alternation Syntax
NM_001363576.1:c.1202C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-07-03
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000012685
ClinVar Disease
Hurler syndrome
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
10738517
Pubmed
1301941
Drugs