Annotation Detail

Information
Associated Genes
F11 F11-AS1
Associated Variants
F11 p.Ser594Arg (p.S594R) ( ENST00000403665.7 )
F11 p.Ser594Arg (p.S594R) ( ENST00000403665.7 )
Associated Disease
Hereditary factor XI deficiency disease
Source Database
ClinVar
Description
NM_000128.4(F11):c.1782C>A (p.Ser594Arg) AND Hereditary factor XI deficiency disease
ClinVar Allele ID
26939
ClinVar RefSeq Alternation Syntax
NR_033900.1:n.976G>T
ClinVar RefSeq Alternation Syntax
NM_000128.4:c.1782C>A
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2021-03-03
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000012675
ClinVar Disease
Hereditary factor XI deficiency disease
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
10606881
Drugs