Annotation Detail

Information
Associated Genes
PRSS1 TRB
Associated Variants
PRSS1 p.Arg122His (p.R122H) ( ENST00000311737.12, ENST00000486171.5, ENST00000492062.2 )
PRSS1 p.Arg122His (p.R122H) ( ENST00000311737.12, ENST00000486171.5, ENST00000492062.2 )
Associated Disease
Hereditary pancreatitis
Source Database
ClinVar
Description
NM_002769.5(PRSS1):c.365_366delinsAT (p.Arg122His) AND Hereditary pancreatitis
ClinVar Allele ID
26921
ClinVar RefSeq Alternation Syntax
NM_002769.5:c.365_366delinsAT
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2006-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000012657
ClinVar Disease
Hereditary pancreatitis
Observed Origin Sample
germline
Observed Origin Sample
inherited
Pubmed
16791840
Pubmed
11702203
Drugs