Annotation Detail

Information
Associated Genes
PRSS1 TRB
Associated Variants
PRSS1 p.Asn29Ile (p.N29I) ( ENST00000311737.12, ENST00000486171.5, ENST00000492062.2 )
PRSS1 p.Asn29Ile (p.N29I) ( ENST00000311737.12, ENST00000486171.5, ENST00000492062.2 )
Associated Disease
Hereditary pancreatitis
Source Database
ClinVar
Description
NM_002769.5(PRSS1):c.86A>T (p.Asn29Ile) AND Hereditary pancreatitis
ClinVar Allele ID
26916
ClinVar RefSeq Alternation Syntax
NM_002769.5:c.86A>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-10-24
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000012652
ClinVar Disease
Hereditary pancreatitis
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
9322498
Pubmed
6023921
Pubmed
10204851
Pubmed
10909845
Drugs