Annotation Detail

Information
Associated Genes
PRSS1 TRB
Associated Variants
PRSS1 p.Arg122His (p.R122H) ( ENST00000486171.5, ENST00000492062.2, ENST00000311737.12 )
PRSS1 p.Arg122His (p.R122H) ( ENST00000311737.12, ENST00000486171.5, ENST00000492062.2 )
Associated Disease
Hereditary pancreatitis
Source Database
ClinVar
Description
NM_002769.5(PRSS1):c.365G>A (p.Arg122His) AND Hereditary pancreatitis
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
12413370
Pubmed
11938439
Pubmed
16791840
Pubmed
12765848
Pubmed
11702203
Pubmed
8841182
Pubmed
10204851
ClinVar Allele ID
26915
ClinVar RefSeq Alternation Syntax
NM_002769.5:c.365G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-11-25
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000012651
ClinVar Disease
Hereditary pancreatitis
Drugs