Annotation Detail

Information
Associated Genes
GJB1
Associated Variants
GJB1 p.Glu102Ter (p.E102*) ( ENST00000361726.7, ENST00000374029.2, ENST00000447581.2, ENST00000645009.2, ENST00000646835.1, ENST00000647424.1, ENST00000674549.1, ENST00000674844.1, ENST00000675209.1, ENST00000675368.1, ENST00000675609.1 )
GJB1 p.Glu102Ter (p.E102*) ( ENST00000361726.7, ENST00000374029.2, ENST00000447581.2, ENST00000645009.2, ENST00000646835.1, ENST00000647424.1, ENST00000674549.1, ENST00000674844.1, ENST00000675209.1, ENST00000675368.1, ENST00000675609.1 )
Associated Disease
Charcot-Marie-Tooth disease X-linked dominant 1
Source Database
ClinVar
Description
NM_000166.6(GJB1):c.304G>T (p.Glu102Ter) AND Charcot-Marie-Tooth disease X-linked dominant 1
ClinVar Allele ID
625575
ClinVar RefSeq Alternation Syntax
NM_000166.6:c.304G>T
ClinVar RefSeq Alternation Syntax
NM_001097642.3:c.304G>T
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2016-01-06
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000011188
ClinVar Disease
Charcot-Marie-Tooth disease X-linked dominant 1
Observed Origin Sample
germline
Pubmed
10487913
Drugs