Annotation Detail

Information
Associated Genes
G6PD
Associated Variants
G6PD p.Asn126Asp (p.N126D) ( ENST00000369620.6, ENST00000393562.10, ENST00000393564.7, ENST00000439227.6, ENST00000696420.1, ENST00000696421.1, ENST00000696429.1, ENST00000696430.1 )
G6PD p.Val68Met (p.V68M) ( ENST00000369620.6, ENST00000393562.10, ENST00000393564.7, ENST00000439227.6, ENST00000696420.1, ENST00000696421.1, ENST00000696429.1, ENST00000696430.1 )
G6PD p.Asn126Asp (p.N126D) ( ENST00000369620.6, ENST00000393562.10, ENST00000393564.7, ENST00000439227.6, ENST00000696420.1, ENST00000696421.1, ENST00000696429.1, ENST00000696430.1 )
G6PD p.Val68Met (p.V68M) ( ENST00000369620.6, ENST00000393562.10, ENST00000393564.7, ENST00000439227.6, ENST00000696420.1, ENST00000696421.1, ENST00000696429.1, ENST00000696430.1 )
Associated Disease
G6PD deficiency
Source Database
ClinVar
Description
G6PD A- AND G6PD deficiency
ClinVar Allele ID
25400
ClinVar Allele ID
25399
ClinVar RefSeq Alternation Syntax
NM_000402.4:c.466A>G
ClinVar RefSeq Alternation Syntax
NM_000402.4:c.292G>A
ClinVar RefSeq Alternation Syntax
NM_001042351.3:c.202G>A
ClinVar RefSeq Alternation Syntax
NM_001360016.2:c.202G>A
ClinVar RefSeq Alternation Syntax
NM_001042351.3:c.376A>G
ClinVar RefSeq Alternation Syntax
NM_001360016.2:c.376A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2000-03-31
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000011075
ClinVar Disease
G6PD deficiency
Observed Origin Sample
germline
Pubmed
669721
Pubmed
7106752
Pubmed
7291768
Pubmed
4388132
Pubmed
2912886
Pubmed
2253938
Pubmed
5492291
Pubmed
2572288
Pubmed
10734064
Pubmed
5448
Pubmed
2503817
Pubmed
1303173
Pubmed
1978554
Pubmed
903703
Pubmed
3393536
Pubmed
2836867
Drugs