Annotation Detail

Information
Associated Genes
CDKN2A
Associated Variants
CDKN2A p.Ala76CysfsTer64 (p.A76Cfs*64) ( ENST00000304494.10, ENST00000479692.2, ENST00000494262.5, ENST00000497750.1, ENST00000498124.1, ENST00000498628.6, ENST00000530628.2, ENST00000578845.2, ENST00000579122.1, ENST00000579755.2 )
CDKN2A p.Ala76CysfsTer64 (p.A76Cfs*64) ( ENST00000304494.10, ENST00000479692.2, ENST00000494262.5, ENST00000497750.1, ENST00000498124.1, ENST00000498628.6, ENST00000530628.2, ENST00000578845.2, ENST00000579122.1, ENST00000579755.2 )
Associated Disease
Melanoma-pancreatic cancer syndrome
Source Database
ClinVar
Description
NM_000077.5(CDKN2A):c.226_244del (p.Ala76fs) AND Melanoma-pancreatic cancer syndrome
ClinVar Allele ID
24449
ClinVar RefSeq Alternation Syntax
NM_001195132.2:c.226_244del
ClinVar RefSeq Alternation Syntax
NM_058195.4:c.269_287del
ClinVar RefSeq Alternation Syntax
NM_001363763.2:c.73_91del
ClinVar RefSeq Alternation Syntax
NM_058197.5:c.*149_*167del
ClinVar RefSeq Alternation Syntax
NM_000077.5:c.226_244del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2012-06-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000010015
ClinVar Disease
Melanoma-pancreatic cancer syndrome
Observed Origin Sample
unknown
Pubmed
7670475
Pubmed
22636603
Pubmed
10956390
Pubmed
10400925
Pubmed
12549483
Drugs