Annotation Detail

Information
Associated Genes
SCN5A LOC110121269
Associated Variants
SCN5A p.Ser1103Tyr (p.S1103Y) ( ENST00000333535.9, ENST00000413689.6, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
SCN5A p.Ser1103Tyr (p.S1103Y) ( ENST00000333535.9, ENST00000413689.6, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
Associated Disease
sudden infant death syndrome
Source Database
ClinVar
Description
NM_000335.5(SCN5A):c.3305C>A (p.Ser1102Tyr) AND SUDDEN INFANT DEATH SYNDROME
ClinVar Allele ID
24432
ClinVar RefSeq Alternation Syntax
NM_001160160.2:c.3305C>A
ClinVar RefSeq Alternation Syntax
NM_198056.3:c.3308C>A
ClinVar RefSeq Alternation Syntax
NM_000335.5:c.3305C>A
ClinVar RefSeq Alternation Syntax
NM_001099405.2:c.3308C>A
ClinVar RefSeq Alternation Syntax
NM_001099404.2:c.3308C>A
ClinVar RefSeq Alternation Syntax
NM_001354701.2:c.3305C>A
ClinVar RefSeq Alternation Syntax
NM_001160161.2:c.3228+1515C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2008-04-15
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000009993
ClinVar Disease
SUDDEN INFANT DEATH SYNDROME
Observed Origin Sample
germline
Pubmed
12193783
Pubmed
12471205
Pubmed
15851227
Pubmed
16453024
Pubmed
18378609
Drugs