Annotation Detail

Information
Associated Genes
KRT2
Associated Variants
KRT2 p.Asn186Lys (p.N186K) ( ENST00000309680.4 )
KRT2 p.Asn186Lys (p.N186K) ( ENST00000309680.4 )
Associated Disease
Ichthyosis bullosa of Siemens
Source Database
ClinVar
Description
NM_000423.3(KRT2):c.558C>A (p.Asn186Lys) AND Ichthyosis bullosa of Siemens
ClinVar Allele ID
24355
ClinVar RefSeq Alternation Syntax
NM_000423.3:c.558C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2001-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000009901
ClinVar Disease
Ichthyosis bullosa of Siemens
Observed Origin Sample
germline
Pubmed
11531804
Drugs