Annotation Detail

Information
Associated Genes
KRT2
Associated Variants
KRT2 p.Glu487Lys (p.E487K) ( ENST00000309680.4 )
KRT2 p.Glu487Lys (p.E487K) ( ENST00000309680.4 )
Associated Disease
Exfoliative ichthyosis
Source Database
ClinVar
Description
NM_000423.3(KRT2):c.1459G>A (p.Glu487Lys) AND Exfoliative ichthyosis
ClinVar Allele ID
24349
ClinVar RefSeq Alternation Syntax
NM_000423.3:c.1459G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1999-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000009895
ClinVar Disease
Exfoliative ichthyosis
Observed Origin Sample
germline
Pubmed
7524919
Pubmed
10233323
Pubmed
8077693
Pubmed
7521371
Pubmed
2004005
Drugs