Annotation Detail

Information
Associated Genes
CASR
Associated Variants
CASR p.Cys592Tyr (p.C592Y) ( ENST00000490131.7, ENST00000498619.4, ENST00000638421.1, ENST00000639785.2 )
CASR p.Cys592Tyr (p.C592Y) ( ENST00000490131.7, ENST00000498619.4, ENST00000638421.1, ENST00000639785.2 )
Associated Disease
Neonatal severe primary hyperparathyroidism
Source Database
ClinVar
Description
NM_000388.4(CASR):c.1745G>A (p.Cys582Tyr) AND Neonatal severe primary hyperparathyroidism
ClinVar Allele ID
23357
ClinVar RefSeq Alternation Syntax
NM_000388.4:c.1745G>A
ClinVar RefSeq Alternation Syntax
NM_001178065.2:c.1775G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1995-12-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000008819
ClinVar Disease
Neonatal severe primary hyperparathyroidism
Observed Origin Sample
germline
Pubmed
8675635
Drugs