Annotation Detail

Information
Associated Genes
RAPSN
Associated Variants
RAPSN p.Asn88Lys (p.N88K) ( ENST00000298854.7, ENST00000529341.1, ENST00000352508.7, ENST00000524487.5 )
RAPSN p.Asn88Lys (p.N88K) ( ENST00000298854.7, ENST00000352508.7, ENST00000524487.5, ENST00000529341.1 )
Associated Disease
congenital myasthenic syndrome 4C
Source Database
ClinVar
Description
NM_005055.5(RAPSN):c.264C>A (p.Asn88Lys) AND Congenital myasthenic syndrome 4C
ClinVar Allele ID
23085
ClinVar RefSeq Alternation Syntax
NM_005055.5:c.264C>A
ClinVar RefSeq Alternation Syntax
NM_032645.5:c.264C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-01-17
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000008512
ClinVar Disease
Congenital myasthenic syndrome 4C
Observed Origin Sample
germline
Drugs