Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Leu1940Pro (p.L1940P) ( ENST00000370225.4 )
ABCA4 p.Leu1940Pro (p.L1940P) ( ENST00000370225.4 )
Associated Disease
Severe early-childhood-onset retinal dystrophy
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.5819T>C (p.Leu1940Pro) AND Severe early-childhood-onset retinal dystrophy
ClinVar Allele ID
22950
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.5597T>C
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.5819T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2008-07-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000008371
ClinVar Disease
Severe early-childhood-onset retinal dystrophy
Observed Origin Sample
germline
Pubmed
18285826
Pubmed
11385708
Drugs