Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Glu616AspfsTer33 (p.E616Dfs*33) ( ENST00000370225.4, ENST00000649773.1 )
ABCA4 p.Glu616AspfsTer33 (p.E616Dfs*33) ( ENST00000370225.4, ENST00000649773.1 )
Associated Disease
retinitis pigmentosa 19
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.1848del (p.Glu616fs) AND Retinitis pigmentosa 19
ClinVar Allele ID
22928
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.1847delA
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.1848del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1998-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000008342
ClinVar Disease
Retinitis pigmentosa 19
Observed Origin Sample
germline
Pubmed
9425888
Pubmed
9070931
Drugs