Annotation Detail

Information
Associated Genes
TGFBI
Associated Variants
TGFBI p.Gly623Asp (p.G623D) ( ENST00000442011.7, ENST00000508076.5 )
TGFBI p.Gly623Asp (p.G623D) ( ENST00000442011.7, ENST00000508076.5 )
Associated Disease
Reis-Bucklers' corneal dystrophy
Source Database
ClinVar
Description
NM_000358.3(TGFBI):c.1868G>A (p.Gly623Asp) AND Reis-Bucklers' corneal dystrophy
ClinVar Allele ID
22915
ClinVar RefSeq Alternation Syntax
NM_000358.3:c.1868G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2005-06-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000008325
ClinVar Disease
Reis-Bucklers' corneal dystrophy
Observed Origin Sample
germline
Pubmed
15885785
Pubmed
11146721
Drugs