Annotation Detail

Information
Associated Genes
CFTR LOC111674475
Associated Variants
CFTR p.Gly551Ser (p.G551S) ( ENST00000003084.11, ENST00000648260.1, ENST00000649406.1, ENST00000649781.2, ENST00000699602.1, ENST00000699605.1 )
CFTR p.Gly551Ser (p.G551S) ( ENST00000003084.11, ENST00000648260.1, ENST00000649406.1, ENST00000649781.2, ENST00000699602.1, ENST00000699605.1 )
Associated Disease
cystic fibrosis
Source Database
ClinVar
Description
NM_000492.4(CFTR):c.1651G>A (p.Gly551Ser) AND Cystic fibrosis
ClinVar Allele ID
22181
ClinVar RefSeq Alternation Syntax
NM_000492.4:c.1651G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-03-17
Clinical Significance Review Status
reviewed by expert panel
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000007562
ClinVar Disease
Cystic fibrosis
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
1944451
Drugs