Annotation Detail

Information
Associated Genes
LMX1B
Associated Variants
LMX1B p.Gln82Ter (p.Q82*) ( ENST00000355497.10, ENST00000373474.9, ENST00000526117.6 )
LMX1B p.Gln82Ter (p.Q82*) ( ENST00000355497.10, ENST00000373474.9, ENST00000526117.6 )
Associated Disease
nail-patella syndrome
Source Database
ClinVar
Description
NM_001174147.2(LMX1B):c.244C>T (p.Gln82Ter) AND Nail-patella syndrome
ClinVar Allele ID
22044
ClinVar RefSeq Alternation Syntax
NM_001174147.2:c.244C>T
ClinVar RefSeq Alternation Syntax
NM_001174146.2:c.244C>T
ClinVar RefSeq Alternation Syntax
NM_002316.4:c.244C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1998-07-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000007420
ClinVar Disease
Nail-patella syndrome
Observed Origin Sample
germline
Pubmed
9618165
Drugs