Annotation Detail

Information
Associated Genes
TP63
Associated Variants
TP63 p.Ser580Pro (p.S580P) ( ENST00000264731.8, ENST00000320472.9, ENST00000354600.10, ENST00000392460.7, ENST00000392461.7, ENST00000392463.6, ENST00000440651.6, ENST00000449992.5, ENST00000456148.1 )
TP63 p.Ser580Pro (p.S580P) ( ENST00000264731.8, ENST00000320472.9, ENST00000354600.10, ENST00000392460.7, ENST00000392461.7, ENST00000392463.6, ENST00000440651.6, ENST00000449992.5, ENST00000456148.1 )
Associated Disease
Rapp-Hodgkin ectodermal dysplasia syndrome
Source Database
ClinVar
Description
NM_003722.5(TP63):c.1738T>C (p.Ser580Pro) AND Rapp-Hodgkin ectodermal dysplasia syndrome
ClinVar Allele ID
21584
ClinVar RefSeq Alternation Syntax
NM_001329145.2:c.1226-3332T>C
ClinVar RefSeq Alternation Syntax
NM_001114980.2:c.1456T>C
ClinVar RefSeq Alternation Syntax
NM_001329149.2:c.1214-3332T>C
ClinVar RefSeq Alternation Syntax
NM_001114981.2:c.1370+1390T>C
ClinVar RefSeq Alternation Syntax
NM_001329146.2:c.1201T>C
ClinVar RefSeq Alternation Syntax
NM_001329150.2:c.959-3332T>C
ClinVar RefSeq Alternation Syntax
NM_001329148.2:c.1726T>C
ClinVar RefSeq Alternation Syntax
NM_001329964.2:c.1732T>C
ClinVar RefSeq Alternation Syntax
NM_003722.5:c.1738T>C
ClinVar RefSeq Alternation Syntax
NM_001114978.2:c.1652+1390T>C
ClinVar RefSeq Alternation Syntax
NM_001329144.2:c.1508-3332T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2003-06-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000006920
ClinVar Disease
Rapp-Hodgkin ectodermal dysplasia syndrome
Observed Origin Sample
germline
Pubmed
12766194
Drugs