Annotation Detail

Information
Associated Genes
TP63
Associated Variants
TP63 p.Cys561Gly (p.C561G) ( ENST00000264731.8, ENST00000320472.9, ENST00000354600.10, ENST00000392460.7, ENST00000392461.7, ENST00000392463.6, ENST00000440651.6, ENST00000449992.5, ENST00000456148.1 )
TP63 p.Cys561Gly (p.C561G) ( ENST00000264731.8, ENST00000320472.9, ENST00000354600.10, ENST00000392460.7, ENST00000392461.7, ENST00000392463.6, ENST00000440651.6, ENST00000449992.5, ENST00000456148.1 )
Associated Disease
ankyloblepharon-ectodermal defects-cleft lip/palate syndrome
Source Database
ClinVar
Description
NM_003722.5(TP63):c.1681T>G (p.Cys561Gly) AND Ankyloblepharon-ectodermal defects-cleft lip/palate syndrome
ClinVar Allele ID
21575
ClinVar RefSeq Alternation Syntax
NM_001329144.2:c.1508-3389T>G
ClinVar RefSeq Alternation Syntax
NM_001114978.2:c.1652+1333T>G
ClinVar RefSeq Alternation Syntax
NM_001329148.2:c.1669T>G
ClinVar RefSeq Alternation Syntax
NM_001329145.2:c.1226-3389T>G
ClinVar RefSeq Alternation Syntax
NM_001329964.2:c.1675T>G
ClinVar RefSeq Alternation Syntax
NM_001329150.2:c.959-3389T>G
ClinVar RefSeq Alternation Syntax
NM_001114981.2:c.1370+1333T>G
ClinVar RefSeq Alternation Syntax
NM_001329149.2:c.1214-3389T>G
ClinVar RefSeq Alternation Syntax
NM_001329146.2:c.1144T>G
ClinVar RefSeq Alternation Syntax
NM_001114980.2:c.1399T>G
ClinVar RefSeq Alternation Syntax
NM_003722.5:c.1681T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2001-02-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000006910
ClinVar Disease
Ankyloblepharon-ectodermal defects-cleft lip/palate syndrome
Observed Origin Sample
germline
Pubmed
9774969
Pubmed
11159940
Drugs