Annotation Detail

Information
Associated Genes
TFR2 LOC113687175
Associated Variants
TFR2 p.Gln690Pro (p.Q690P) ( ENST00000223051.8, ENST00000431692.5, ENST00000462107.1 )
TFR2 p.Gln690Pro (p.Q690P) ( ENST00000223051.8, ENST00000431692.5, ENST00000462107.1 )
Associated Disease
hemochromatosis type 3
Source Database
ClinVar
Description
NM_003227.4(TFR2):c.2069A>C (p.Gln690Pro) AND Hemochromatosis type 3
ClinVar Allele ID
20423
ClinVar RefSeq Alternation Syntax
NM_001206855.3:c.1556A>C
ClinVar RefSeq Alternation Syntax
NM_003227.4:c.2069A>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2002-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000005715
ClinVar Disease
Hemochromatosis type 3
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
12130528
Drugs