Annotation Detail

Information
Associated Genes
TFR2
Associated Variants
TFR2 p.Tyr250Ter (p.Y250*) ( ENST00000223051.8, ENST00000431692.5, ENST00000462107.1 )
TFR2 p.Tyr250Ter (p.Y250*) ( ENST00000223051.8, ENST00000431692.5, ENST00000462107.1 )
Associated Disease
hemochromatosis type 3
Source Database
ClinVar
Description
NM_003227.4(TFR2):c.750C>G (p.Tyr250Ter) AND Hemochromatosis type 3
ClinVar Allele ID
20419
ClinVar RefSeq Alternation Syntax
NM_003227.4:c.750C>G
ClinVar RefSeq Alternation Syntax
NM_001206855.3:c.237C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2000-05-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000005711
ClinVar Disease
Hemochromatosis type 3
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
10802645
Drugs