Annotation Detail

Information
Associated Genes
TARDBP
Associated Variants
TARDBP p.Gln343Arg (p.Q343R) ( ENST00000700088.1, ENST00000621790.4, ENST00000240185.8, ENST00000629725.2, ENST00000649624.1, ENST00000315091.7, ENST00000616545.4, ENST00000639083.1 )
TARDBP p.Gln343Arg (p.Q343R) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
Associated Disease
amyotrophic lateral sclerosis type 10
Source Database
ClinVar
Description
NM_007375.4(TARDBP):c.1028A>G (p.Gln343Arg) AND Amyotrophic lateral sclerosis type 10
ClinVar Allele ID
20274
ClinVar RefSeq Alternation Syntax
NM_007375.4:c.1028A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2008-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000005546
ClinVar Disease
Amyotrophic lateral sclerosis type 10
Observed Origin Sample
germline
Pubmed
18438952
Drugs