Annotation Detail

Information
Associated Genes
WFS1
Associated Variants
WFS1 p.Lys634Thr (p.K634T) ( ENST00000226760.5, ENST00000506362.2, ENST00000503569.5, ENST00000673991.1, ENST00000682275.1, ENST00000684087.1 )
WFS1 p.Lys634Thr (p.K634T) ( ENST00000226760.5, ENST00000503569.5, ENST00000506362.2, ENST00000673991.1, ENST00000682275.1, ENST00000684087.1 )
Associated Disease
Autosomal dominant nonsyndromic hearing loss 6
Source Database
ClinVar
Description
NM_006005.3(WFS1):c.1901A>C (p.Lys634Thr) AND Autosomal dominant nonsyndromic hearing loss 6
ClinVar Allele ID
19563
ClinVar RefSeq Alternation Syntax
NM_001145853.1:c.1901A>C
ClinVar RefSeq Alternation Syntax
NM_006005.3:c.1901A>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2002-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000004782
ClinVar Disease
Autosomal dominant nonsyndromic hearing loss 6
Observed Origin Sample
germline
Pubmed
9817917
Pubmed
8595423
Pubmed
12181639
Drugs