Annotation Detail

Information
Associated Genes
PKHD1
Associated Variants
PKHD1 p.Val3471Gly (p.V3471G) ( ENST00000371117.8 )
PKHD1 p.Val3471Gly (p.V3471G) ( ENST00000371117.8 )
Associated Disease
autosomal recessive polycystic kidney disease
Source Database
ClinVar
Description
NM_138694.4(PKHD1):c.10412T>G (p.Val3471Gly) AND Autosomal recessive polycystic kidney disease
ClinVar Allele ID
19154
ClinVar RefSeq Alternation Syntax
NM_138694.4:c.10412T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-03-27
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000004331
ClinVar Disease
Autosomal recessive polycystic kidney disease
Observed Origin Sample
germline
Pubmed
12506140
Drugs