Annotation Detail

Information
Associated Genes
KCNQ1
Associated Variants
KCNQ1 p.Val254Met (p.V254M) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
KCNQ1 p.Val417Met (p.V417M) ( ENST00000155840.12, ENST00000496887.7, ENST00000713725.1, ENST00000646564.2, ENST00000335475.6 )
KCNQ1 p.Val254Met (p.V254M) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
KCNQ1 p.Val417Met (p.V417M) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
Associated Disease
long QT syndrome 1
Source Database
ClinVar
Description
NM_000218.2(KCNQ1):c.[1249G>A;760G>A] AND Long QT syndrome 1
ClinVar Allele ID
18157
ClinVar Allele ID
38428
ClinVar RefSeq Alternation Syntax
NM_000218.3:c.760G>A
ClinVar RefSeq Alternation Syntax
NM_001406837.1:c.490G>A
ClinVar RefSeq Alternation Syntax
NM_000218.3:c.1249G>A
ClinVar RefSeq Alternation Syntax
NM_001406836.1:c.1153G>A
ClinVar RefSeq Alternation Syntax
NM_001406837.1:c.979G>A
ClinVar RefSeq Alternation Syntax
NM_181798.2:c.379G>A
ClinVar RefSeq Alternation Syntax
NM_001406836.1:c.760G>A
ClinVar RefSeq Alternation Syntax
NM_181798.2:c.868G>A
ClinVar RefSeq Alternation Syntax
NM_001406838.1:c.709G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2004-03-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000003296
ClinVar Disease
Long QT syndrome 1
Observed Origin Sample
germline
Pubmed
14756674
Drugs