Annotation Detail

Information
Associated Genes
ATM
Associated Variants
ATM p.Asp1682His (p.D1682H) ( ENST00000452508.7, ENST00000278616.10, ENST00000601453.3, ENST00000675843.1, ENST00000713844.1 )
ATM p.Asp1682His (p.D1682H) ( ENST00000278616.10, ENST00000452508.7, ENST00000601453.3, ENST00000675843.1, ENST00000713844.1 )
Associated Disease
T-cell prolymphocytic leukemia
Source Database
ClinVar
Description
NM_000051.4(ATM):c.5044G>C (p.Asp1682His) AND T-cell prolymphocytic leukemia
ClinVar Allele ID
18065
ClinVar RefSeq Alternation Syntax
NM_000051.4:c.5044G>C
ClinVar RefSeq Alternation Syntax
NM_001351834.2:c.5044G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1997-09-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000003165
ClinVar Disease
T-cell prolymphocytic leukemia
Observed Origin Sample
somatic
Pubmed
9288106
Drugs