Annotation Detail

Information
Associated Genes
PCSK9
Associated Variants
PCSK9 p.Phe216Leu (p.F216L) ( ENST00000302118.5, ENST00000673903.1, ENST00000710286.1, ENST00000713786.1 )
PCSK9 p.Phe216Leu (p.F216L) ( ENST00000302118.5, ENST00000673903.1, ENST00000710286.1, ENST00000713786.1 )
Associated Disease
Hypercholesterolemia, autosomal dominant, 3
Source Database
ClinVar
Description
NM_174936.4(PCSK9):c.646T>C (p.Phe216Leu) AND Hypercholesterolemia, autosomal dominant, 3
ClinVar Allele ID
17913
ClinVar RefSeq Alternation Syntax
NM_001407245.1:c.454T>C
ClinVar RefSeq Alternation Syntax
NM_001407243.1:c.589T>C
ClinVar RefSeq Alternation Syntax
NM_001407244.1:c.646T>C
ClinVar RefSeq Alternation Syntax
NM_001407246.1:c.271T>C
ClinVar RefSeq Alternation Syntax
NM_001407247.1:c.646T>C
ClinVar RefSeq Alternation Syntax
NM_174936.4:c.646T>C
ClinVar RefSeq Alternation Syntax
NM_001407240.1:c.769T>C
ClinVar RefSeq Alternation Syntax
NM_001407241.1:c.646T>C
ClinVar RefSeq Alternation Syntax
NM_001407242.1:c.646T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2008-02-12
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000003008
ClinVar Disease
Hypercholesterolemia, autosomal dominant, 3
Observed Origin Sample
germline
Pubmed
12730697
Pubmed
18250299
Drugs